Knowledge Graph Extraction from Biomedical Literature for Alkaptonuria Rare Disease

Fuente: arXiv
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Main Authors: Pham, Giang, Finetti, Rebecca, Graziani, Caterina, Roncaglia, Bianca, Bendjeddou, Asma, Brodo, Linda, Brunetti, Sara, Falaschi, Moreno, Forti, Stefano, Galfré, Silvia Giulia, Milazzo, Paolo, Priami, Corrado, Santucci, Annalisa, Spiga, Ottavia, Sîrbu, Alina
Format: Preprint
Published: 2026
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author Pham, Giang
Finetti, Rebecca
Graziani, Caterina
Roncaglia, Bianca
Bendjeddou, Asma
Brodo, Linda
Brunetti, Sara
Falaschi, Moreno
Forti, Stefano
Galfré, Silvia Giulia
Milazzo, Paolo
Priami, Corrado
Santucci, Annalisa
Spiga, Ottavia
Sîrbu, Alina
author_facet Pham, Giang
Finetti, Rebecca
Graziani, Caterina
Roncaglia, Bianca
Bendjeddou, Asma
Brodo, Linda
Brunetti, Sara
Falaschi, Moreno
Forti, Stefano
Galfré, Silvia Giulia
Milazzo, Paolo
Priami, Corrado
Santucci, Annalisa
Spiga, Ottavia
Sîrbu, Alina
contents Alkaptonuria (AKU) is an ultra-rare autosomal recessive metabolic disorder caused by mutations in the HGD (Homogentisate 1,2-Dioxygenase) gene, leading to a pathological accumulation of homogentisic acid (HGA) in body fluids and tissues. This leads to systemic manifestations, including premature spondyloarthropathy, renal and prostatic stones, and cardiovascular complications. Being ultra-rare, the amount of data related to the disease is limited, both in terms of clinical data and literature. Knowledge graphs (KGs) can help connect the limited knowledge about the disease (basic mechanisms, manifestations and existing therapies) with other knowledge; however, AKU is frequently underrepresented or entirely absent in existing biomedical KGs. In this work, we apply a text-mining methodology based on PubTator3 for large-scale extraction of biomedical relations. We construct two KGs of different sizes, validate them using existing biochemical knowledge and use them to extract genes, diseases and therapies possibly related to AKU. This computational framework reveals the systemic interactions of the disease, its comorbidities, and potential therapeutic targets, demonstrating the efficacy of our approach in analyzing rare metabolic disorders.
format Preprint
id arxiv_https___arxiv_org_abs_2603_15711
institution arXiv
publishDate 2026
record_format arxiv
spellingShingle Knowledge Graph Extraction from Biomedical Literature for Alkaptonuria Rare Disease
Pham, Giang
Finetti, Rebecca
Graziani, Caterina
Roncaglia, Bianca
Bendjeddou, Asma
Brodo, Linda
Brunetti, Sara
Falaschi, Moreno
Forti, Stefano
Galfré, Silvia Giulia
Milazzo, Paolo
Priami, Corrado
Santucci, Annalisa
Spiga, Ottavia
Sîrbu, Alina
Artificial Intelligence
Information Retrieval
Quantitative Methods
Alkaptonuria (AKU) is an ultra-rare autosomal recessive metabolic disorder caused by mutations in the HGD (Homogentisate 1,2-Dioxygenase) gene, leading to a pathological accumulation of homogentisic acid (HGA) in body fluids and tissues. This leads to systemic manifestations, including premature spondyloarthropathy, renal and prostatic stones, and cardiovascular complications. Being ultra-rare, the amount of data related to the disease is limited, both in terms of clinical data and literature. Knowledge graphs (KGs) can help connect the limited knowledge about the disease (basic mechanisms, manifestations and existing therapies) with other knowledge; however, AKU is frequently underrepresented or entirely absent in existing biomedical KGs. In this work, we apply a text-mining methodology based on PubTator3 for large-scale extraction of biomedical relations. We construct two KGs of different sizes, validate them using existing biochemical knowledge and use them to extract genes, diseases and therapies possibly related to AKU. This computational framework reveals the systemic interactions of the disease, its comorbidities, and potential therapeutic targets, demonstrating the efficacy of our approach in analyzing rare metabolic disorders.
title Knowledge Graph Extraction from Biomedical Literature for Alkaptonuria Rare Disease
topic Artificial Intelligence
Information Retrieval
Quantitative Methods
url https://arxiv.org/abs/2603.15711