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Gmppb-mutant mice exhibit dystroglycanopathy symptoms that are rescued with GSK3β inhibition or AAV-mediated GMPPB gene replacement.

Fuente: PubMed

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Bibliographic Details
Main Authors:	Fu, Ziwei, Wang, Tongchao, Zhang, Chenyang, Qi, Tianyu, Chen, Yanyan, Yang, Ju, Yang, Hua, Yan, Bing, Gong, Baoming, Lu, Weiqiao, Luo, Sushan, Liu, Ying, Sun, Lei, Jiang, Hao, Chen, Bo, Zhang, Zhao, Liu, Xiuping, Wang, Yuxiang
Format:	Artículo científico
Language:	en
Published:	Nature communications 2026
Subjects:	Animals Female Mice Male Dystroglycans Nucleotidyltransferases Glycogen Synthase Kinase 3 beta Mice, Knockout Mutation Muscle, Skeletal Wnt Signaling Pathway Glycosylation Disease Models, Animal Muscular Dystrophies
Online Access:	Acceder al recurso
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