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| Formato: | Artículo científico |
| Lenguaje: | en |
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Universidad del Valle
2015
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| Acceso en línea: | https://www.redalyc.org/articulo.oa?id=28338620008 https://www.redalyc.org/journal/283/28338620008/ https://www.redalyc.org/journal/283/28338620008/html/ https://www.redalyc.org/journal/283/28338620008/28338620008.epub https://www.redalyc.org/journal/283/28338620008/movil |
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| _version_ | 1866817029604900864 |
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| author | Andrés Felipe Zea-Vera |
| author_facet | Andrés Felipe Zea-Vera |
| contents | Disseminated bronchiectasis in an adult with common variable immunodeficiency Andrés Felipe Zea-Vera Olga Lucia Agudelo-Rojas Medicina bronchiectasis recurring pneumonia hypogammaglobulinemia Primary immunodeficiency (PID) common variable immunodeficiency (CVID) Primary immunodeficiencies (PID) are traditionally considered childhood diseases; however, adults account for 35% of all patients with PID. Antibody deficiencies, especially Common Variable Immunodeficiency (CVID), which have their peak incidence in adulthood, require a high suspicion index. Even though the estimated frequency of CVID is not high (1:25,000), high rates of under diagnosis and under reporting are very likely. The delay in diagnosis increases the morbidity and mortality; therefore, adult physicians should be able to suspect, identify and initiate management of individuals with PID. Here we report the case of a 37 year-old man presenting to the emergency room with dyspnea, fever and cough; he developed respiratory failure requiring mechanical ventilation. He complained of recurring pneumonia associated with widespread bronchiectasis since he was 18 years old. Serum immunoglobulins quantification showed severe hypogammaglobulinemia (total IgG <140 mg/dL; total IgA, 2.9 mg/dL; and total IgM <5 mg/dL). Treatment with Human Intravenous Immunoglobulin (IVIG) 10% was started, and with antibiotic treatment for severe pneumonia (during 14 days) was also prescribed. His clinical evolution has been favorable after one year follow-up. Common Variable Immunodeficiency (CVID) diagnosis was made. 2015 artículo científico 0120-8322 https://www.redalyc.org/articulo.oa?id=28338620008 https://www.redalyc.org/journal/283/28338620008/ https://www.redalyc.org/journal/283/28338620008/html/ https://www.redalyc.org/journal/283/28338620008/28338620008.epub https://www.redalyc.org/journal/283/28338620008/movil en http://www.redalyc.org/revista.oa?id=283 Colombia Médica application/pdf Universidad del Valle Colombia Médica (Colombia) Num.1 Vol.46 |
| format | Artículo científico |
| id | redalyc_28338620008 |
| language | en |
| publishDate | 2015 |
| publisher | Universidad del Valle |
| spellingShingle | Disseminated bronchiectasis in an adult with common variable immunodeficiency Andrés Felipe Zea-Vera Medicina bronchiectasis recurring pneumonia hypogammaglobulinemia Primary immunodeficiency (PID) common variable immunodeficiency (CVID) Disseminated bronchiectasis in an adult with common variable immunodeficiency Andrés Felipe Zea-Vera Olga Lucia Agudelo-Rojas Medicina bronchiectasis recurring pneumonia hypogammaglobulinemia Primary immunodeficiency (PID) common variable immunodeficiency (CVID) Primary immunodeficiencies (PID) are traditionally considered childhood diseases; however, adults account for 35% of all patients with PID. Antibody deficiencies, especially Common Variable Immunodeficiency (CVID), which have their peak incidence in adulthood, require a high suspicion index. Even though the estimated frequency of CVID is not high (1:25,000), high rates of under diagnosis and under reporting are very likely. The delay in diagnosis increases the morbidity and mortality; therefore, adult physicians should be able to suspect, identify and initiate management of individuals with PID. Here we report the case of a 37 year-old man presenting to the emergency room with dyspnea, fever and cough; he developed respiratory failure requiring mechanical ventilation. He complained of recurring pneumonia associated with widespread bronchiectasis since he was 18 years old. Serum immunoglobulins quantification showed severe hypogammaglobulinemia (total IgG <140 mg/dL; total IgA, 2.9 mg/dL; and total IgM <5 mg/dL). Treatment with Human Intravenous Immunoglobulin (IVIG) 10% was started, and with antibiotic treatment for severe pneumonia (during 14 days) was also prescribed. His clinical evolution has been favorable after one year follow-up. Common Variable Immunodeficiency (CVID) diagnosis was made. 2015 artículo científico 0120-8322 https://www.redalyc.org/articulo.oa?id=28338620008 https://www.redalyc.org/journal/283/28338620008/ https://www.redalyc.org/journal/283/28338620008/html/ https://www.redalyc.org/journal/283/28338620008/28338620008.epub https://www.redalyc.org/journal/283/28338620008/movil en http://www.redalyc.org/revista.oa?id=283 Colombia Médica application/pdf Universidad del Valle Colombia Médica (Colombia) Num.1 Vol.46 |
| title | Disseminated bronchiectasis in an adult with common variable immunodeficiency |
| topic | Medicina bronchiectasis recurring pneumonia hypogammaglobulinemia Primary immunodeficiency (PID) common variable immunodeficiency (CVID) |
| url | https://www.redalyc.org/articulo.oa?id=28338620008 https://www.redalyc.org/journal/283/28338620008/ https://www.redalyc.org/journal/283/28338620008/html/ https://www.redalyc.org/journal/283/28338620008/28338620008.epub https://www.redalyc.org/journal/283/28338620008/movil |