Enfermedad de Castleman multicéntrica hialina vascular. Una variante de POEMS
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| Format: | Artículo científico |
| Language: | es |
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Instituto Mexicano del Seguro Social
2013
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| author | Abraham Edgar Gracia-Ramos |
| author_facet | Abraham Edgar Gracia-Ramos |
| contents | Enfermedad de Castleman multicéntrica hialina vascular. Una variante de POEMS Abraham Edgar Gracia-Ramos María del Pilar Cruz-Domínguez Olga Lidia Vera-Lastra Medicina POEMS syndrome giant lymph node hyperplasia Background: Castleman’s disease is an atypical lymphoproliferative disorder which may be compatible with paraneoplastic manifestations of POEMS syndrome.Clinical case: a 53 year old man with a history of type 2 diabetes, hypothyroidism and Addison’s disease was attended. He started with numbness and weakness in limbs, dyspnea, skin hardening, Rayn-aud’s phenomenon, weight loss and fatigue appeared. Physical exam showed tachypnea, generalized cutaneous hyperpigmentation and skin hardening of extremities, muscle weakness, hypoesthesia and hypore-fl exia. Laboratory showed hyperprolactinemia, low testosterone, hypo-thyroidism and Addison’s disease. Electrophoresis of proteins showed polyclonal hypergammaglobulinemia. Somatosensory evoked potentials reported peripheral neuropathy and severe axonal polyneuropathy by electromyography. Chest X-rays showed bilateral reticular infi ltrates and mediastinal widening. Echocardiogram displayed moderate pulmonary hypertension. Skin biopsy had no evidence of scleroderma. CT reported axillar, mediastinal and retroperitoneal nodes. The mediastinal lesion biopsy reported hyaline vascular Castleman’s disease, multicentric vari-ety. He was treated with rituximab. Conclusions: the case meet criteria for multicentric hyaline vascular Castleman’s disease, POEMS variant, treated with rituximab. 2013 artículo científico 0443-5117 https://www.redalyc.org/articulo.oa?id=457745490021 es http://www.redalyc.org/revista.oa?id=4577 Revista Médica del Instituto Mexicano del Seguro Social application/pdf Instituto Mexicano del Seguro Social Revista Médica del Instituto Mexicano del Seguro Social (México) Num.4 Vol.51 |
| format | Artículo científico |
| id | redalyc_457745490021 |
| institution | Redalyc |
| language | es |
| publishDate | 2013 |
| publisher | Instituto Mexicano del Seguro Social |
| spellingShingle | Enfermedad de Castleman multicéntrica hialina vascular. Una variante de POEMS Abraham Edgar Gracia-Ramos Medicina POEMS syndrome giant lymph node hyperplasia Enfermedad de Castleman multicéntrica hialina vascular. Una variante de POEMS Abraham Edgar Gracia-Ramos María del Pilar Cruz-Domínguez Olga Lidia Vera-Lastra Medicina POEMS syndrome giant lymph node hyperplasia Background: Castleman’s disease is an atypical lymphoproliferative disorder which may be compatible with paraneoplastic manifestations of POEMS syndrome.Clinical case: a 53 year old man with a history of type 2 diabetes, hypothyroidism and Addison’s disease was attended. He started with numbness and weakness in limbs, dyspnea, skin hardening, Rayn-aud’s phenomenon, weight loss and fatigue appeared. Physical exam showed tachypnea, generalized cutaneous hyperpigmentation and skin hardening of extremities, muscle weakness, hypoesthesia and hypore-fl exia. Laboratory showed hyperprolactinemia, low testosterone, hypo-thyroidism and Addison’s disease. Electrophoresis of proteins showed polyclonal hypergammaglobulinemia. Somatosensory evoked potentials reported peripheral neuropathy and severe axonal polyneuropathy by electromyography. Chest X-rays showed bilateral reticular infi ltrates and mediastinal widening. Echocardiogram displayed moderate pulmonary hypertension. Skin biopsy had no evidence of scleroderma. CT reported axillar, mediastinal and retroperitoneal nodes. The mediastinal lesion biopsy reported hyaline vascular Castleman’s disease, multicentric vari-ety. He was treated with rituximab. Conclusions: the case meet criteria for multicentric hyaline vascular Castleman’s disease, POEMS variant, treated with rituximab. 2013 artículo científico 0443-5117 https://www.redalyc.org/articulo.oa?id=457745490021 es http://www.redalyc.org/revista.oa?id=4577 Revista Médica del Instituto Mexicano del Seguro Social application/pdf Instituto Mexicano del Seguro Social Revista Médica del Instituto Mexicano del Seguro Social (México) Num.4 Vol.51 |
| title | Enfermedad de Castleman multicéntrica hialina vascular. Una variante de POEMS |
| topic | Medicina POEMS syndrome giant lymph node hyperplasia |
| url | https://www.redalyc.org/articulo.oa?id=457745490021 |