Congenital cystic adenomatoid malformation type I

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Auteur principal: Alice Rebelo de Matos Borges dos Reis
Format: Artículo científico
Langue:en
Publié: Hospital Universitário da Universidade de São Paulo 2015
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author Alice Rebelo de Matos Borges dos Reis
author_facet Alice Rebelo de Matos Borges dos Reis
contents Congenital cystic adenomatoid malformation type I Alice Rebelo de Matos Borges dos Reis Frederico Becker Ribeiro Regina Schultz Medicina Autopsy Prognosis Congenital Classification CysticAdenomatoid Malformation of Lung Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature male newborn with the prenatal diagnosis of CCAM Type 1 associated with cardiac right axis deviation, who died 67 hours after birth due to respiratory failure. In addition to the autopsy report of this rare entity, the authors present its classification and prognosis. 2015 artículo científico 2236-1960 https://www.redalyc.org/articulo.oa?id=576060830004 en http://www.redalyc.org/revista.oa?id=5760 Autopsy and Case Reports application/pdf Hospital Universitário da Universidade de São Paulo Autopsy and Case Reports (Brasil) Num.3 Vol.5
format Artículo científico
id redalyc_576060830004
institution Redalyc
language en
publishDate 2015
publisher Hospital Universitário da Universidade de São Paulo
spellingShingle Congenital cystic adenomatoid malformation type I
Alice Rebelo de Matos Borges dos Reis
Medicina
Autopsy
Prognosis
Congenital
Classification
CysticAdenomatoid Malformation of Lung
Congenital cystic adenomatoid malformation type I Alice Rebelo de Matos Borges dos Reis Frederico Becker Ribeiro Regina Schultz Medicina Autopsy Prognosis Congenital Classification CysticAdenomatoid Malformation of Lung Congenital cystic adenomatoid malformation (CCAM) is an hamartomatous congenital pulmonary airway malformation with incidence ranging between 1:10,000 and 1:35,000 newborns. Currently CCAM is classified into five groups according to clinical and pathological features. The clinical outcome varies depending on the subtype and the extent of involvement. The authors report the case of a premature male newborn with the prenatal diagnosis of CCAM Type 1 associated with cardiac right axis deviation, who died 67 hours after birth due to respiratory failure. In addition to the autopsy report of this rare entity, the authors present its classification and prognosis. 2015 artículo científico 2236-1960 https://www.redalyc.org/articulo.oa?id=576060830004 en http://www.redalyc.org/revista.oa?id=5760 Autopsy and Case Reports application/pdf Hospital Universitário da Universidade de São Paulo Autopsy and Case Reports (Brasil) Num.3 Vol.5
title Congenital cystic adenomatoid malformation type I
topic Medicina
Autopsy
Prognosis
Congenital
Classification
CysticAdenomatoid Malformation of Lung
url https://www.redalyc.org/articulo.oa?id=576060830004