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| Main Author: | |
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| Format: | Artículo científico |
| Language: | en |
| Published: |
Hospital Universitário da Universidade de São Paulo
2022
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| Subjects: | |
| Online Access: | https://www.redalyc.org/articulo.oa?id=576069818042 https://www.redalyc.org/journal/5760/576069818042/ https://www.redalyc.org/journal/5760/576069818042/html/ https://www.redalyc.org/journal/5760/576069818042/576069818042.epub https://www.redalyc.org/journal/5760/576069818042/movil |
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Table of Contents:
- Vertebrobasilar circulation hemorrhages in childhood primary angiitis of the central nervous system Ahmad Hassan Kieren Allinson Medicina Autopsy Diagnosis Mortality Vasculitis Brain Death Childhood primary angiitis of the CNS (cPACNS) is a poorly understood, rare, and diagnostically challenging neurologic disease. We describe an unusual and autopsy-confirmed case of cPACNS presenting as vertebrobasilar circulation hemorrhagic strokes in a 4-year-old girl. The presentation and clinical features were inconsistent with primary CNS vasculitis and skewed the diagnosis. Autopsy and histopathological analyses revealed a progressive lymphocytic vasculitis affecting the medium to large vessels of vertebrobasilar circulation and sparing the anterior circulation. It is imperative to raise the index of suspicion for cPACNS in any case of unusual or unexplained neurological presentation, especially in the absence of cerebrovascular risk factors and/or coagulation disorders. 2022 otro 2236-1960 https://www.redalyc.org/articulo.oa?id=576069818042 https://www.redalyc.org/journal/5760/576069818042/ https://www.redalyc.org/journal/5760/576069818042/html/ https://www.redalyc.org/journal/5760/576069818042/576069818042.epub https://www.redalyc.org/journal/5760/576069818042/movil 10.4322/acr.2021.391 en http://www.redalyc.org/revista.oa?id=5760 Autopsy and Case Reports application/pdf Hospital Universitário da Universidade de São Paulo Autopsy and Case Reports (Brasil) Vol.12