A case of severe cutaneous involvement on initial clinical presentation of juvenile dermatomyositis

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Autor principal: Teresa Cristina Martins Vicente Robazzi
Formato: Artículo científico
Lenguaje:en
Publicado: Sociedad Argentina de Reumatología 2015
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author Teresa Cristina Martins Vicente Robazzi
author_facet Teresa Cristina Martins Vicente Robazzi
contents A case of severe cutaneous involvement on initial clinical presentation of juvenile dermatomyositis Teresa Cristina Martins Vicente Robazzi Celina Bulhões Leandra Chaves Cristiani Leal Medicina clinical presentation Juvenile dermatomyositis Juvenile dermatomyositis is an autoimmune vasculopathy affecting children and adolescents, principally between the ages of four and 16 years. Its main clinical manifestations aresymmetrical proximal muscle weakness, elevated serum muscle enzymes and the presenceof cutaneous lesions, such as heliotrope and Gottron’s papules. Herein we describe a caseof juvenile dermatomyositis with a precocious time of onset at 18 months of age, notablypresenting with severe ulcerative cutaneous lesions and vasculopathy likely due to gastrointestinal involvement, which required immediates. treatment with immunosuppressant. 2015 artículo científico 0327-4411 https://www.redalyc.org/articulo.oa?id=692177050004 en http://www.redalyc.org/revista.oa?id=6921 Revista Argentina de Reumatología application/pdf Sociedad Argentina de Reumatología Revista Argentina de Reumatología (Argentina) Num.3 Vol.26
format Artículo científico
id redalyc_692177050004
institution Redalyc
language en
publishDate 2015
publisher Sociedad Argentina de Reumatología
spellingShingle A case of severe cutaneous involvement on initial clinical presentation of juvenile dermatomyositis
Teresa Cristina Martins Vicente Robazzi
Medicina
clinical presentation
Juvenile dermatomyositis
A case of severe cutaneous involvement on initial clinical presentation of juvenile dermatomyositis Teresa Cristina Martins Vicente Robazzi Celina Bulhões Leandra Chaves Cristiani Leal Medicina clinical presentation Juvenile dermatomyositis Juvenile dermatomyositis is an autoimmune vasculopathy affecting children and adolescents, principally between the ages of four and 16 years. Its main clinical manifestations aresymmetrical proximal muscle weakness, elevated serum muscle enzymes and the presenceof cutaneous lesions, such as heliotrope and Gottron’s papules. Herein we describe a caseof juvenile dermatomyositis with a precocious time of onset at 18 months of age, notablypresenting with severe ulcerative cutaneous lesions and vasculopathy likely due to gastrointestinal involvement, which required immediates. treatment with immunosuppressant. 2015 artículo científico 0327-4411 https://www.redalyc.org/articulo.oa?id=692177050004 en http://www.redalyc.org/revista.oa?id=6921 Revista Argentina de Reumatología application/pdf Sociedad Argentina de Reumatología Revista Argentina de Reumatología (Argentina) Num.3 Vol.26
title A case of severe cutaneous involvement on initial clinical presentation of juvenile dermatomyositis
topic Medicina
clinical presentation
Juvenile dermatomyositis
url https://www.redalyc.org/articulo.oa?id=692177050004