PRUNE BELLY SYNDROME: A CASE REPORT
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2025
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| _version_ | 1866901750210887680 |
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| author | Fatima Mbarki , Khadija Skalli , Driss Oukachou and Fouzia Hmami |
| author_facet | Fatima Mbarki , Khadija Skalli , Driss Oukachou and Fouzia Hmami |
| contents | <p>Prune Belly Syndrome (PBS) is a rare congenital malformation that primarily affects boys. It is characterized by hypoplasia of the abdominal wall muscles, urological anomalies, and bilateral cryptorchidism. Although the etiology remains unclear, genetic factors and chromosomal abnormalities are suspected. Early diagnosis is essential, as the prognosis ranges from unfavorable to near-normal survival. We report the case of a premature neonate diagnosed with PBS at birth, who required surgical intervention but unfortunately passed away at 8 months due to urinary tract infections and severe dehydration. A multidisciplinaryapproachis crucial to improve patient outcomes.</p> <p> </p> |
| format | Recurso digital |
| id | zenodo_https___doi_org_10_21474_IJAR01_20447 |
| institution | Zenodo |
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| publishDate | 2025 |
| publisher | Zenodo |
| record_format | zenodo |
| spellingShingle | PRUNE BELLY SYNDROME: A CASE REPORT Fatima Mbarki , Khadija Skalli , Driss Oukachou and Fouzia Hmami Prune Belly Syndrome Abdominal Wall Musculature Deficiency Bilateral Cryptorchidism Urinary Tract Anomalies <p>Prune Belly Syndrome (PBS) is a rare congenital malformation that primarily affects boys. It is characterized by hypoplasia of the abdominal wall muscles, urological anomalies, and bilateral cryptorchidism. Although the etiology remains unclear, genetic factors and chromosomal abnormalities are suspected. Early diagnosis is essential, as the prognosis ranges from unfavorable to near-normal survival. We report the case of a premature neonate diagnosed with PBS at birth, who required surgical intervention but unfortunately passed away at 8 months due to urinary tract infections and severe dehydration. A multidisciplinaryapproachis crucial to improve patient outcomes.</p> <p> </p> |
| title | PRUNE BELLY SYNDROME: A CASE REPORT |
| topic | Prune Belly Syndrome Abdominal Wall Musculature Deficiency Bilateral Cryptorchidism Urinary Tract Anomalies |
| url | https://doi.org/10.21474/IJAR01/20447 |