Sub-trochanteric Femoral Fracture in a Young Hemophilia A Patient and its Management

Fuente: Zenodo
Salvato in:
Dettagli Bibliografici
Autori principali: Ali, Abdul Basit, Muhammad, Usman
Natura: Recurso digital
Lingua:inglese
Pubblicazione: Zenodo 2024
Soggetti:
Accesso online:
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne!!
_version_ 1866902024610643968
author Ali, Abdul Basit
Muhammad, Usman
author_facet Ali, Abdul Basit
Muhammad, Usman
contents <p><strong><span>Introduction</span></strong></p> <p><span>Hemophilia is an X linked recessive chromosomal bleeding disorder in which there is an anomaly in synthesis of clotting factors. These patients experience heavy episodes of bleeding even from minor cuts. Hemophilia is a condition of great interest for orthopedic surgeons due to its clinical manifestations.<span>  </span>Our aim is to present a case of hemophilia A with proximal femoral fracture and its management.</span></p> <p><strong><span>Case presentation</span></strong></p> <p><span>An eighteen-year-old boy with Hemophilia A, who presented after a road traffic accident at a hospital, where he was managed by fresh frozen plasma (FFP) and blood transfusion. His treatment was delayed due to unavailability of factor VIII at hospital and his family arranged it on their own. His surgery planned after 2 days of admission, internal fixation by cephalomedullary nailing was done.</span></p> <p><strong><span>Discussion </span></strong></p> <p><span>Hemophilia diagnosis involves a combination of factor VIII level assays and abnormal bleeding episodes in the patient. The treatment involves prophylactic administration of factor VIII. In case of femoral fractures in these patients, intramedullary nailing is preferred while maintaining the levels of factor VIII at the same time.</span></p> <p><strong><span>Conclusion</span></strong></p> <p><span>Management of fracture in this hemophilia patient was a difficult task. Early presentation at the hospital had a positive while unavailability of recombinant factor VIII concentrate on time had a negative impact on the outcome.</span></p>
format Recurso digital
id zenodo_https___doi_org_10_5281_zenodo_14000627
institution Zenodo
language eng
publishDate 2024
publisher Zenodo
record_format zenodo
spellingShingle Sub-trochanteric Femoral Fracture in a Young Hemophilia A Patient and its Management
Ali, Abdul Basit
Muhammad, Usman
Hemophilia, Subtrochanteric fractures, Intramedullary nailing, Factor VIII, Blood clotting.
<p><strong><span>Introduction</span></strong></p> <p><span>Hemophilia is an X linked recessive chromosomal bleeding disorder in which there is an anomaly in synthesis of clotting factors. These patients experience heavy episodes of bleeding even from minor cuts. Hemophilia is a condition of great interest for orthopedic surgeons due to its clinical manifestations.<span>  </span>Our aim is to present a case of hemophilia A with proximal femoral fracture and its management.</span></p> <p><strong><span>Case presentation</span></strong></p> <p><span>An eighteen-year-old boy with Hemophilia A, who presented after a road traffic accident at a hospital, where he was managed by fresh frozen plasma (FFP) and blood transfusion. His treatment was delayed due to unavailability of factor VIII at hospital and his family arranged it on their own. His surgery planned after 2 days of admission, internal fixation by cephalomedullary nailing was done.</span></p> <p><strong><span>Discussion </span></strong></p> <p><span>Hemophilia diagnosis involves a combination of factor VIII level assays and abnormal bleeding episodes in the patient. The treatment involves prophylactic administration of factor VIII. In case of femoral fractures in these patients, intramedullary nailing is preferred while maintaining the levels of factor VIII at the same time.</span></p> <p><strong><span>Conclusion</span></strong></p> <p><span>Management of fracture in this hemophilia patient was a difficult task. Early presentation at the hospital had a positive while unavailability of recombinant factor VIII concentrate on time had a negative impact on the outcome.</span></p>
title Sub-trochanteric Femoral Fracture in a Young Hemophilia A Patient and its Management
topic Hemophilia, Subtrochanteric fractures, Intramedullary nailing, Factor VIII, Blood clotting.
url https://doi.org/10.5281/zenodo.14000627